Tuberc Respir Dis.  1995 Aug;42(4):600-604.

A Case of Pulmonary and Retroperitoneal Lymphangioleiomyomatosis

• Kwak NJ
• Park NG
• Kim HY
• Eom JH
• Choi MC
• Yun SJ
• Kim ST
• Do Lee S

Abstract

Lymphangioleiomyomatosis, a rare disease in women of childbearing age, is the result of benign nodular hypertrophy of the smooth muscle of the lypmhatics and other tissues of the abdomen and thorax. We report a 36-years-old woman with pulmonary and retroperitoneal lymphangioleiomyomatosis who responded with hormone treatment. She developed vaginal pruritis and a pelvic ultraound was done given her significant past medical history. Ultrasound examination demonstrated a large mass in the right side of her pelvis. Therefore she was admitted to St. Michael's Hospital in Toronto for laparoscopy. Result of cytology was to be consistent with the diagnosis of retroperitoneal lymphangioleiomyomatosis. High resolution CT sacn of the thorax demonstrated multiple small cystic lesions, without associated nodularity compatible with a diagnosis of pulmonary lymphangioleiomyomatosis. She has been taking Provera tablets l00mg po tid since Dec. 15, 1993. We have given her a prescription for Depo provera 500mg IM monthly since she came back to Korea, and made arrangements for regular follow up monthly. We performed chest X-ray, CT of chest(high resolution), abdomen and pelvis, pulmonary function tests and arterial blood gas analysis. Chest X-ray and CT findings showed no significant change since July. 20, 1993.

Keyword

Pulmonary; Retroperitoneal Lymphangioleiomyomatosis

MeSH Terms

Abdomen
Blood Gas Analysis
Diagnosis
Female
Follow-Up Studies
Humans
Hypertrophy
Korea
Laparoscopy
Lymphangioleiomyomatosis*
Medroxyprogesterone Acetate
Muscle, Smooth
Pelvis
Prescriptions
Pruritus
Rare Diseases
Respiratory Function Tests
Tablets
Thorax
Ultrasonography
Medroxyprogesterone Acetate
Tablets