Korean J Dermatol.
2003 Jun;41(6):820-822.
A Case of Segmental Neurofibromatosis
- Affiliations
-
- 1Department of Dermatology, College of Medicine, Dongguk University, Kyongju, Korea. mksuhmd@hanmail.net
- 2Department of Pathology, College of Medicine, Dongguk University, Kyongju, Korea.
Abstract
- Segmental neurofibromatosis(neurofibromatosis type V) is rare disorder characterized by limitation of cafe-au-lait spots and neurofibroma or only neurofibroma on a given unilateral segment of the body. We report a case of segmental neurofibromatosis that developed in a 58-year-old male. The skin lesion was situated on the right antecubital area and wrist in the distribution of dermatomes C5 and C6. Histopathologic examination showed well-demarcated, non-encapsulated tumor of the dermis was composed of thin wavy collagenous fibers and loosely spaced spindle cells with elongated wavy nuclei. The patient was treated with surgical excision and carbon dioxide laser.
