Ann Dermatol.  2003 Dec;15(4):156-159. 10.5021/ad.2003.15.4.156.

Bilateral Segmental Neurofibromatosis with Partial Unilateral Lentiginosis: Case Report with Review of the Literature

• Kim YJ
• Kim MY
• Kim HO
• Park YM

• KMID: 2171846
• DOI: http://doi.org/10.5021/ad.2003.15.4.156

Abstract

Bilateral segmental neurofibromatosis is a rare disease characterized by bilateral neurofibromas, with or without pigmented lesion, or unilateral neurofibromas with contralateral pigmented lesion, limited to a body segment. Partial unilateral lentiginosis is characterized by numerous lentigines localized to a body segment, often corresponding to one or more dermatome. Bilateral segmental neurofibromatosis combined with partial unilateral lentiginosis is very rare, and to our knowledge, only 2 cases have been reported in English literature. We herein report another case of bilateral segmental neurofibromatosis with partial unilateral lentiginosis in a 46-year-old woman.

Keyword

Bilateral segmental neurofibromatosis; Partial unilateral lentiginosis

MeSH Terms

Female
Humans
Lentigo*
Middle Aged
Neurofibroma
Neurofibromatoses*
Neurofibromatosis 1
Rare Diseases