Korean J Thorac Cardiovasc Surg.  2004 Apr;37(4):364-368.

Congenital Pulmonary Vein Stenosis with Normal Anatomical Connection: One case report

Affiliations
  • 1Department of Thoracic and Cardiovascular Surgery, Samsung Seoul Hospital, Sungkyunkwan University School of Medicine, Korea. tgjun@smc.samsung.co.kr
  • 2Sejong Heart Institute, Sejong General Hospital, Korea.
  • 3Department of Pediatrics, Samsung Seoul Hospital, Sungkyunkwan University School of Medicine, Korea.

Abstract

Congenital pulmonary vein stenosis is a rare anomaly and related to high mortality due to progressive pulmonary hypertension and heart failure in infancy. Aggressive anti-failure medication and surgical treatment is recommended. Surgical options are balloon dilatation, endovascular stent, pneumonectomy, lung transplantation, patch grafting, and sutureless repair. We report a case of congenital pulmonary vein stenosis with normal anatomical connection successfully treated with sutureless technique and using pulmonary vasodilators, such as Sildenafil, Iloprost and iNO postoperatively.

Keyword

Pulmonary veins; Suture; Surgery method; Congenital heart defect

MeSH Terms

Constriction, Pathologic*
Dilatation
Heart Defects, Congenital
Heart Failure
Hypertension, Pulmonary
Iloprost
Lung Transplantation
Mortality
Pneumonectomy
Pulmonary Veins*
Stents
Sutures
Transplants
Vasodilator Agents
Sildenafil Citrate
Iloprost
Vasodilator Agents
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