Korean J Spine.  2015 Sep;12(3):169-172. 10.14245/kjs.2015.12.3.169.

Idiopathic Hypertrophic Pachymeningitis in the Craniocervical Junction

• Bang JH
• Cho KT
• Kim EJ

• KMID: 2288343
• DOI: http://doi.org/10.14245/kjs.2015.12.3.169

Abstract

Idiopathic hypertrophic pachymeningitis (IHP) is a rare disease, and it is characterized by chronic progressive inflammatory fibrosis and thickening of the dura mater with resultant compression of the spinal cord or neural structure without any identifiable cause. It can occur in the intracranial or spinal dura mater alone or as a craniospinal form. The spinal form is rarer than the cranial form and the craniospinal form is extremely rare. We report a rare case of IHP in the craniocervical junction involving both the cranial and spinal dura mater and discuss the diagnosis and management of the disease.

Keyword

Idiopathic hypertrophic pachymeningitis; Craniocervical junction; Diagnosis; Treatment

MeSH Terms

Diagnosis
Dura Mater
Fibrosis
Meningitis*
Rare Diseases
Spinal Cord