Korean J Otorhinolaryngol-Head Neck Surg.  2012 Mar;55(3):188-190. 10.3342/kjorl-hns.2012.55.3.188.

A Case of Intratympanic Membrane Congenital Cholesteatoma

• Kim YH

• KMID: 2277341
• DOI: http://doi.org/10.3342/kjorl-hns.2012.55.3.188

Abstract

Intratympanic membrane congenital cholesteatoma (ITMCC) is extremely rare in patients without previous trauma or surgery of the ear. There are multiple theories to the pathogenesis of middle ear congenital cholesteatoma but none are applicable for ITMCC. When the size of ITMCC is small, there are usually no ear symptoms. However, surgery is needed early, as in any other type of cholesteatoma, because early treatment before middle ear involvement enables enucleation without the need for other procedures such as myringoplasty. We report an incidental finding of a small pearl at the umbo in a 2-year-old boy. The cholesteatoma involved only the outer epidermic layer of the tympanic membrane (TM). A transcanal approach was performed and the cholesteatoma was enucleated from TM.

Keyword

Tympanic membrane; Congenital; Cholesteatoma

MeSH Terms

Cholesteatoma
Ear
Ear, Middle
Humans
Incidental Findings
Membranes
Myringoplasty
Preschool Child
Tympanic Membrane