Korean J Med.  2013 Jan;84(1):85-90.

Severe Pulmonary Hypertension Caused by Pulmonary Artery Stenosis in a Patient with Behcet's Disease Treated by Balloon Angioplasty

• Kim KR
• Kim HJ
• Kim MS
• Bae SK
• Kim HS
• Hur KH
• Kang DW

Abstract

Pulmonary artery stenosis that causes pulmonary hypertension is usually observed in congenital anomalies and is seldom observed in adults. A 47-year-old female patient came to the hospital for aggravated dyspnea and peripheral edema. Severe pulmonary hypertension was found on an echocardiography examination, along with dilation of the main pulmonary artery and alias flow at the bifurcation sites of both pulmonary arteries. Under coronary angio-computed tomography, 70% high grade stenosis was observed on both sides of the proximal pulmonary arteries without showing atherosclerotic plaque or a thrombus. The patient's symptoms improved after performing pulmonary artery angiography and angioplasty. Thus, we report our experience of a patient with Behcet's disease and severe pulmonary hypertension caused by pulmonary artery stenosis, which was treated with percutaneous pulmonary angioplasty.

Keyword

Behcet's disease; Pulmonary artery stenosis; Pulmonary hypertension; Pulmonary artery angioplasty

MeSH Terms

Adult
Angiography
Angioplasty
Angioplasty, Balloon
Constriction, Pathologic
Dyspnea
Echocardiography
Edema
Female
Humans
Hypertension, Pulmonary
Plaque, Atherosclerotic
Porphyrins
Pulmonary Artery
Thrombosis
Porphyrins