Ann Rehabil Med.  2014 Dec;38(6):852-855. 10.5535/arm.2014.38.6.852.

Churg-Strauss Syndrome Presented With Hearing Impairment and Facial Palsy

• Byun JH
• Lee JH
• Choi IS

• KMID: 2267098
• DOI: http://doi.org/10.5535/arm.2014.38.6.852

Abstract

Churg-Strauss syndrome (CSS) is a rare systemic necrotizing vasculitis. Cranial nerve involvement is very rare in CSS. A 59-year-old woman had complained of both hearing impairments for eight months and left facial palsy for three months. Left facial and cochlear neuropathies were detected in electrodiagnostic studies. Paranasal sinus computed tomography (CT) showed chronic pansinusitis. Chest CT revealed eosinophilic infiltration in the right upper lobe. Tissue biopsy of the right inferior turbinate displayed necrotizing vasculitis with eosinophilic infiltration. She was diagnosed as CSS, based on the presence of eosinophilia, pulmonary infiltration, paranasal sinusitis, and biopsy containing blood vessels with extravascular eosinophils. She was treated with intravenous and oral steroids and azathioprine, showing relatively good prognosis on facial palsy and hearing impairment. We report a very rare case of CSS presented with hearing impairment and facial palsy.

Keyword

Churg-Strauss syndrome; Facial paralysis; Hearing loss

MeSH Terms

Azathioprine
Biopsy
Blood Vessels
Churg-Strauss Syndrome*
Cranial Nerves
Eosinophils
Facial Paralysis*
Female
Hearing
Hearing Loss*
Humans
Middle Aged
Prognosis
Pulmonary Eosinophilia
Sinusitis
Steroids
Tomography, X-Ray Computed
Turbinates
Vasculitis
Azathioprine
Steroids

Figure

• 

  Fig. 1 Paranasal sinus computed tomography showed chronic pansinusitis (arrow head) and diffuse soft tissue thickening (arrow).

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  Fig. 2 Chest computed tomography displayed a nodule with surrounding ground-glass opacity in the right upper lobe (arrow).

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  Fig. 3 Tissue biopsy of right inferior turbinate revealed eosinophilic infiltration (arrows).

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