Korean J Nephrol.
2010 Jul;29(4):519-524.
Immunoglobulin G4 Related Retroperitoneal Fibrosis with Acute Kidney Injury: Report of A Case
- Affiliations
-
- 1Department of Internal Medicine, College of Medicine, University of Ulsan, Asan Medical Center, Seoul, Korea. jwchang@amc.seoul.kr
- 2Department of Pathology, College of Medicine, University of Ulsan, Asan Medical Center, Seoul, Korea.
- 3Department of Internal Medicine, College of Medicine, Dankook University, Cheonan, Korea.
- 4Department of Internal Medicine, College of Medicine, Cheju National University, Cheju, Korea.
Abstract
- Immunoglobuin G4 (IgG4)-related sclerosing disease is a recently recognized syndrome characterized clinically by male predominance, elevated serum IgG4 level, and good response to steroid therapy. The pathologic characteristics are extensive lymphoplasmacytic infiltration with IgG4-positive cell and irregular fibrosis in various organs (pancreas, bile duct, salivary gland, retroperitoneum, kidney and lung). Some inflammatory pseudotumors may be involved in this disease. Herein, we experienced a case of IgG4-related retroperitoneal fibrosis with postrenal acute kidney injury and inflammatory pseudotumor of thyroid in a 31-year-old female who underwent insertion of double J catheter at both ureters and received corticosteroid treatment.