Korean J Anesthesiol.  2007 Oct;53(4):535-538. 10.4097/kjae.2007.53.4.535.

Airway Management in a Patient with Goldenhar's Syndrome: A case report

• Lee WK
• Kim EJ
• Lee JH
• Lee SG
• Ban JS
• Min BW

• KMID: 2236608
• DOI: http://doi.org/10.4097/kjae.2007.53.4.535

Abstract

Goldenhar's syndrome is a rare form of a hemifacial microsomia in which the facial and vertebral anomalies are frequently associated with cardiac, pulmonary and renal defects. Infants with Goldenhar's syndrome commonly have an airway that is difficulty to manage. A difficult tracheal intubation may be due to a combination of mandibular hypoplasia, macrognathia, palatal defects and vertebral anomalies. We report the successful anesthetic management of a 10-month-old girl with Goldenhar's syndrome for the excision of conjunctival lipodermoid. The use of remifentanil followed with an anesthetic induction dose of propofol provides adequate conditions for tracheal intubation without the use of neuromuscluar blocking agents in a patient with Goldenhar's syndrome.

Keyword

Goldenhar's syndrome; propofol; remifentanil

MeSH Terms

Airway Management*
Female
Goldenhar Syndrome
Humans
Infant
Intubation
Propofol
Propofol