Korean J Dermatol.  1993 Aug;31(4):616-619.

A case of Maffucci's syndrome

• Won JH
• Hur W
• Choi EH
• Hann SK

Abstract

Maffucci's syndrome is a congenital, non-hereditary mesodermal d splasia manifested by multiple enchondromas and hemangiomas. Several case reports and reviews indicate that there is a tendency toward malignant transformation of the enchondroma. The incidence of malignancy may be as high as 30%. We report a case of 10-year-old female with multiple hemangiomas on the face, palms, and soles and skeletal chondromatoses of the multiple bones.

Keyword

Maffuccis Syndrorne; Enchondroma; Hemangioma

MeSH Terms

Child
Chondroma
Chondromatosis
Enchondromatosis
Female
Hemangioma
Humans
Incidence
Mesoderm