Korean J Dermatol.  1987 Aug;25(4):546-552.

A Case of angioimmunoblastic Lymphadenopathy with Dysproteinemia

• Kim HJ
• Kim YK
• Pyo HC

Abstract

We present a case of angioimmunoblastic lymphadenopathy with dysproteinemia (AILD) in a 57-year-old male who had suffered from fever and general weakness of one month's duration. He showed generalized lymphadenopathy, hepatomegaly and purpuric maculopapules on the whole body surface. Lahoratory findings show anemia, polyclonal gammaglobulinemia and thrombocytopenia. The lymph node biopsy specimens show morphologic triad of AILD except lack of interstitial deposits of eosinophilic materials and the skin biopsy specimen shows lymphohistiocytic vasculitis. Bone marrow biopsy specimen shows similar findings in lymph node, suggesting bone marrow involvement. He have been treated with COPP chemotherapy.

Keyword

Angioimmunoblastic lymphadenopathy; Dysproteinemia

MeSH Terms

Anemia
Biopsy
Bone Marrow
Drug Therapy
Eosinophils
Fever
Hepatomegaly
Humans
Immunoblastic Lymphadenopathy*
Lymph Nodes
Lymphatic Diseases
Male
Middle Aged
Skin
Thrombocytopenia
Vasculitis