Korean J Dermatol.  1990 Jun;28(3):362-367.

A Case of Tuberous Sclerosis associated with Angiomyolipoma of Kidney and Regional Lymph Nodes

• Chung Y
• Moon DC
• Kwon KS
• Chung TA

Abstract

In tuberous sclerosis angiomyolipomas involving kidney and regional lymph nodes are known to be extremely rare. We report a 21-year-old female, who has had pinhead-sized reddish or brownish papules on the face and skin colored, orange peel like plaques in the lurnbosacral region. She has suffered from tenderness on the left flank since 4 years ago. Abdominal CT scan revealed a large mass in the upper portion of the left kidney and lymphadenopathy of the para-aortic lymph nodes. Biopsy specimens from the mass of the left kidney and regional lymph nodes revealed angiomyolipomas.

Keyword

Angiomyolipoma; Tuberous sclerosis

MeSH Terms

Angiomyolipoma*
Biopsy
Citrus sinensis
Female
Humans
Kidney*
Lymph Nodes*
Lymphatic Diseases
Skin
Tomography, X-Ray Computed
Tuberous Sclerosis*
Young Adult