Korean J Dermatol.  2000 Sep;38(9):1272-1274.

A Case of Pyogenic Granuloma within Port-Wine Stain Associated with Sturge-Weber Syndrome

• Lee JH
• Park JW
• Lee SY
• Park YL
• Lee JS
• Whang KU

Abstract

Port-wine stains(PWS) are congenital vascular birthmarks and usually isolated but may be associated with other vascular malformations. Sturge-Weber syndrome(SWS) is defined as facial PWS in association with an ipsilateral leptomeningeal vascular malformation, atrophy and calcification of the underlying cerebral cortex, epilepsy, mental retardation, contralateral hemiparesis and ipsilateral choroidal vascular lesions with glaucoma. Pyogenic granulomas or other nodular angiomatous lesions may develop within preexistent vascular malformation such as PWS. We describe a 22 year-old man who developed a pyogenic granuloma within an existing facial PWS associated with SWS.

Keyword

Port-wine stains(PWS); Sturge-Weber syndrome(SWS); Pyogenic granulomas

MeSH Terms

Atrophy
Cerebral Cortex
Choroid
Epilepsy
Glaucoma
Granuloma, Pyogenic*
Humans
Intellectual Disability
Paresis
Port-Wine Stain*
Sturge-Weber Syndrome*
Vascular Malformations
Young Adult