J Rheum Dis.  2013 Feb;20(1):52-55. 10.4078/jrd.2013.20.1.52.

A Case of Behcet's Disease Complicated with a Pulmonary Artery Aneurysm and Deep Vein Thrombosis, Separately

• Lee JM
• Ahn J
• Hwang YJ
• Kim SH
• Lee JS
• Choi SJ
• Lee YH
• Ji JD
• Song GG

• KMID: 2223050
• DOI: http://doi.org/10.4078/jrd.2013.20.1.52

Abstract

Behcet'sdisease is a chronic inflammatory disease characterized by oral ulcers, genital ulcers, uveitis, and skin lesions. Furthermore, Behcet's disease can manifest as vascular lesions, such as, those of vasculitis, venous thrombosis, or thrombophlebitis or as an arterial aneurysm. Here, the authors report the case of a pulmonary artery aneurysm and deep vein thrombosis in a 41-year-old woman with a previous diagnosis of Behcet's disease. The patient presented with hemoptysis and a cough, and was found to have a bleeding pulmonary artery aneurysm at the right lower lung. Pulmonary arteriography was performed and the aneurysm was embolized with coils. As a result, hemoptysis did not subsequently recur. However, five years later, deep vein thrombosis occurred in the left leg. Left leg pain improved after the regional infusion of thrombolytics.

Keyword

Behcet's disease; Pulmonary artery aneurysm; Endovascular embolization; Deep vein thrombosis

MeSH Terms

Aneurysm
Angiography
Cough
Female
Hemoptysis
Hemorrhage
Humans
Leg
Lung
Oral Ulcer
Pulmonary Artery
Skin
Thrombophlebitis
Ulcer
Uveitis
Vasculitis
Venous Thrombosis

Figure

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  Figure 1. Chest X-ray showing ill-defined increased opacity in the right lower lung.

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  Figure 2. Contrast computerized tomography (CT) scan of the thorax showing a round enhancing lesion, measuring 2.2×2.0 cm in size, in the right lower lung (arrow).

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  Figure 3. Pulmonary arteriograph showing Nester coils in the pulmonary artery aneurysm.

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  Figure 4. Lower extremity venograph showing a thrombus in the left popliteal vein and the catheter used for the peripheral venous approach.

Reference

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