J Rheum Dis.  2015 Aug;22(4):246-249. 10.4078/jrd.2015.22.4.246.

A Case of Guillain-Barre Syndrome in a Patient of Behcet's Disease

• Yoo J
• Kim NM
• Sung W
• Myeong JC
• Yun SA
• Lee DK
• Lim MK
• Sheen DH

• KMID: 2222856
• DOI: http://doi.org/10.4078/jrd.2015.22.4.246

Abstract

Behcet's disease (BD) is a multi-systemic inflammatory disease of unknown origin that affects nearly all organs including the nervous system. Although the neurological involvement is less frequent than other major presentations, it is important because it can produce severe disabilities. Peripheral nervous system manifestations are relatively rare in BD. Although few cases of peripheral neuropathy or myopathy have been reported in BD, they are cases of multiple neuropathies, sensorimotor peripheral neuropathy, or neuropathy autonomic dysfunction. Guillain-Barre syndrome (GBS), also known as an acute inflammatory demyelinating polyneuropathy, is an acute demyelinating polyradiculopathy of uncertain etiology. No case of GBS associated with BD in Korea has been reported. Herein we report on a patient of BD who suffered from weakness of extremities and was diagnosed as GBS.

Keyword

Behcet's disease; Guillain-Barre syndrome

MeSH Terms

Extremities
Guillain-Barre Syndrome*
Humans
Korea
Muscular Diseases
Nervous System
Peripheral Nervous System
Peripheral Nervous System Diseases
Polyradiculopathy

Figure

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  Figure 1. Abnormal nerve conduction velocities and F-wave. (A) Motor nerve conduction velocity of right peroneal nerve. (B) Absent F-wave in right peroneal nerve. (C, D) Absent F-wave in both tibial nerves.

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