J Korean Pediatr Soc.
1995 Feb;38(2):275-279.
A Case of Cardiac Tumor Associated with Tuberous Sclerosis in Newborn
- Affiliations
-
- 1Department of Pediatrics, Sung-Ae General Hospital, Seoul, Korea.
- 2Department of Pathology, Seoul National University, College of Medicine, Seoul, Korea.
Abstract
-
Symptomatic primary heart tumors are rare in newborn. Cardiac rhabdomyoma is the most common lesion of the primary heart tumors and over half of them are related to kthe tuberous s clerosis. We described a case of cardiac rhabdomyoma, in a 2 day-old female newborn who presented with dyspnea and cyanosis. A 2D Echocardiogram demonstrated two masses; one is in the rt. ventricle and another is in the interventricular septum. Additional cardiac masses and cerebral tubers and subependymal giant cell astrocytoma were found at autopsy.