Intest Res.
2012 Apr;10(2):210-214. 10.5217/ir.2012.10.2.210.
A Case of Acquired Zonal Aganglionosis in Adult
- Affiliations
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- 1Department of Internal Medicine, Hanyang University College of Medicine, Seoul, Korea. cseun@hanyang.ac.kr
- KMID: 2174245
- DOI: http://doi.org/10.5217/ir.2012.10.2.210
Abstract
- A chronic intestinal pseudo-obstruction is a rare disorder and a severe digestive syndrome. It is characterized by deranged gut propulsive motility that resembles a mechanical obstruction, but no obstructive process is present. An intestinal pseudo-obstruction may be classified as acute or chronic; the chronic form may also be classified as idiopathic or secondary to a variety of diseases. Treatment of intestinal pseudo-obstruction involves nutritional, pharmacological, and surgical therapies. Surgery should be limited to patients who are refractory to medical therapy and show a deteriorating course. Despite available medical and surgical interventions, the outcome remains poor. Here, we describe a case of a 54-year-old female with chronic constipation and abdominal distension, who was subsequently found to have segmental aganglionosis. The patient was treated with a subtotal colectomy and ileosigmoidostomy without sequelae.
