Korean J Perinatol.  2015 Dec;26(4):344-347. 10.14734/kjp.2015.26.4.344.

Fetal Intra-abdominal Umbilical Vein Varix Complicated with Patent Ductus Venosus and Atrial Septal Defect

• Jin HI
• Na MS
• Shin YH
• Lim KA

• KMID: 2164190
• DOI: http://doi.org/10.14734/kjp.2015.26.4.344

Abstract

Umbilical vein varix has diverse clinical features and an unpredictable course during the pregnancy and/or perinatal period. We report a rare case of isolated fetal varix of the intra-abdominal umbilical vein, which was associated with fetal cardiomegaly. After birth, the umbilical vein varix remained with continuous blood flow through the patent ductus venosus. In addition, persistent cardiomegaly was complicated with an atrial septal defect.

Keyword

Umbilical vein varix; Prenatal diagnosis; Patent ductus venosus

MeSH Terms

Cardiomegaly
Heart Septal Defects, Atrial*
Parturition
Pregnancy
Prenatal Diagnosis
Umbilical Veins*
Varicose Veins*

Figure

• 

  Fig. 1. Fetal intra-abdominal umbilical vein varix in a 28-week-old fetus. (A) transverse abdominal view of an obstetrical sonogram showing a hypoechoic tubular structure indicating an umbilical vein varix on the right side of the abdomen at the stomach level (identified on the left side of the abdomen without flow signals). (B) Four-chamber view of the fetus showing an enlarged fetal heart (fetal cardiomegaly), especially in the right atrium.

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  Fig. 2. Remnant of intra-abdominal umbilical vein varix and persistent ductus venosus in a 12-day-old neonate. (A) Oblique view of an abdominal sonogram showing an unusual focally dilated vessel representing a remnant of intra-abdominal umbilical vein varix. (B) Color sonogram revealing continuous blood flow from the dilated vessel into the inferior vena cava just below the insertion of the hepatic veins through the persistent ductus venosus. Abbreviations: HV, hepatic vein; IVC, inferior vena cava; RA, right atrium; UV, umbilical vein.

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  Fig. 3. Anterio-posterior view of chest radiography shows marked cardiomegaly at first day of life.

Reference

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