J Korean Soc Radiol.  2015 Mar;72(3):171-175. 10.3348/jksr.2015.72.3.171.

Multifocal Spinal Hemangioblastoma in von Hippel-Lindau Syndrome: A Case Report and Literature Review

• Kim OH

• KMID: 2161168
• DOI: http://doi.org/10.3348/jksr.2015.72.3.171

Abstract

Hemangioblastoma is a benign vascular neoplasm of the central nervous system that occurs frequently in the cerebellum and other areas of the central nervous system including spinal cord and brainstem. Spinal hemangioblastoma can present as a sporadic isolated lesion or as a component of von Hippel-Lindau syndrome. The author presents a case of 32-year-old man with von Hippel-Lindau syndrome and spinal hemangioblastomas represented by multiple small spinal lesions, with an emphasis on the magnetic resonance imaging findings and clinical characteristics of von Hippel-Lindau syndrome-associated spinal hemangioblastomas.

MeSH Terms

Adult
Brain Stem
Central Nervous System
Cerebellum
Hemangioblastoma*
Humans
Magnetic Resonance Imaging
Spinal Cord
Spinal Cord Neoplasms
Vascular Neoplasms
von Hippel-Lindau Disease*

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