J Korean Neurosurg Soc.  2013 Nov;54(5):415-419. 10.3340/jkns.2013.54.5.415.

Meningeal Supratentorial Hemangioblastoma in a Patient with Von Hippel-Lindau Disease Mimicking Angioblastic Menigioma

• Kim H
• Park IS
• Jo KW

• KMID: 2138358
• DOI: http://doi.org/10.3340/jkns.2013.54.5.415

Abstract

Hemangioblastomas are sporadic tumors found in the cerebellum or spinal cord. Supratentorial hemangioblastomas are rare, and those with meningeal involvement are extremely rare and have been reported in only approximately 130 patients. Here, we report the case of a 51-year-old female patient with supratentorial meningeal hemangioblastoma detected 5 years after surgical resection of an infratentorial hemangioblastoma associated with von Hippel-Lindau disease. Patients with von Hippel-Lindau syndrome are at risk for developing multiple hemangioblastomas, with new tumor formation and growth and possible meningeal infiltration. Regular lifelong follow-up in at-risk patients is recommended and should include the differential diagnosis of dural-based tumors such as angioblastic meningioma and metastatic renal cell carcinoma.

Keyword

Angioblastic meningioma; Hemangioblastoma; Supratentorial; Von Hippel-Lindau disease

MeSH Terms

Carcinoma, Renal Cell
Cerebellum
Diagnosis, Differential
Female
Hemangioblastoma*
Humans
Meningioma
Middle Aged
Spinal Cord
von Hippel-Lindau Disease*