Korean J Gastroenterol.  2014 Dec;64(6):375-379. 10.4166/kjg.2014.64.6.375.

A Case of Low-grade Fibromyxoid Sarcoma of the Colon

• Kim M
• Song TJ
• Kang SD
• Kang JS
• Kim JS
• Lee JS
• Kim CN
• Kim HS

• KMID: 2160671
• DOI: http://doi.org/10.4166/kjg.2014.64.6.375

Abstract

Low-grade fibromyxoid sarcoma is a slowly growing soft tissue neoplasm that shows benign histologic features but may have clinical course of malignant disease. It has been reported to occur in the thigh, inguinal area, axilla, shoulder, neck, perineum or buttock. However, there have been few cases of abdominal organ involvement. A 21-year-old woman presented with a large palpable abdominal mass. A 7x4 cm sized round soft tissue tumor at right upper quadrant area was identified by abdominopelvic CT scan. Percutaneous ultrasound-guided biopsy revealed features of spindle cell tumor. On exploration, the tumor originated from transvers colon and was attached to gastrocolic ligament, transverse mesocolon and stomach. The tumor could be dissected with transverse colectomy and partial gastrectomy. The excised tumor, measuring 7x5x5 cm, was well demarcated and appeared as an ovoid mass with firm and myxoid cut surface. She was diagnosed with low-grade fibromyxoid sarcoma arising from transverse colon, and is currently being followed-up without recurrence or metastasis.

Keyword

Low-grade fibromyxoid sarcoma; Colon; Stomach

MeSH Terms

Colon, Transverse
Female
Humans
S100 Proteins/metabolism
Sarcoma/*diagnosis/pathology/surgery
Soft Tissue Neoplasms/*diagnosis/pathology/surgery
Stomach Neoplasms/pathology/secondary
Tomography, X-Ray Computed
Young Adult
S100 Proteins

Figure

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  Fig. 1. Abdominal computed tomography shows a 7×4 cm sized homogeneous enhancing mass (arrows) between stomach and transvers colon.

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  Fig. 2. Gross pathologic image shows ovoid well demarcated lesion and bisecting surface demonstrates a mixture of yellow colored, mucoid and fibrous tissue.

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  Fig. 3. (A) Transition from fibrous (arrow) to myxoid (asterisk) tumor areas are noted (H&E, ×100). (B) Portion of fibrous tumor reveals arcades of slender blood vessels (H&E, ×100).

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