Korean J Thorac Cardiovasc Surg.
2001 Aug;34(8):626-629.
Congenital Polyvalvular Disease: Report of A Case
- Affiliations
-
- 1Department of Cardiovascular and Thoracic Surgery, Division of Pediatric Cardiac Surgery, Asan Medical Center, Ulsan University, Korea.
- 2Department of Pediatrics, Division of Pediatric Cardiology, Asan Medical Center, Ulsan University, Korea.
- 3Department of Diagnostic Pathology, Asan Medical Center, Ulsan University, Korea.
Abstract
- Congenital polyvavular disease is a connective tissue disorder affecting more than one heart valve with variable involvement of the entire valvular and subvalvular apparatus. It is frequently associated with the Trisomy 18 and trisomy 13-15 or ventricular septal defect and patent ductus arteriosus. We present an isolated case of congenital polyvalvular disease in a new born baby with a review of the pertinent literatures, which has not been described in Korea. The mass was discovered as a right atrial mass in the prenatal ultrasonography and it was thought to be either a hematoma or a myxoma in the preoperative echocardiography. Microscopic examination of the surgically resected mass showed irregular thickening, nodulation, and additional features of calcification and ossification in the valvular connective tissue on the body of anterior and septal leaflet of tricuspid valve. Congenital polyvalvular disease should be included in the differential diagnosis in cases showing valvular calcification or ossification in the fetal echocardiography.
Keyword
- Full Text Links
-
- Actions
-
Cited
- CITED
-
- Close
- Share
-
- Similar articles
-
- Large Congenital Epigastric Hernia with DiGeorge Syndrome: A Case Report
- A Case of Congenital Unilateral Multicystic Kidney with Congenital Megacolon
- Familial Congenital Muscular Torticollis: A Case Report
- Congenital Hemihypertrophy: A case report
- Congenital self-healing reticulohistiocytosis: report of a case of the solitary type and review of the literature
