J Korean Child Neurol Soc.  2001 May;9(1):129-133.

A Case of Suspected Autosomal Dominant Nocturnal Frontal Lobe Epilepsy

• Kim SY
• Park JC
• Kim HD
• Chung HJ

Abstract

Autosomal dominant nocturnal frontal lobe epilepsy(ADNFLE) is a recently identified partial epilepsy. This disorder is characterized by a variable age of onset(mostly in childhood), autosomal dominant inheritance, clusters of brief frontal nocturnal seizures, negative findings on neuroimaging, and fairly good prognosis. Carbamazepine is known to be the most useful drug in this type of epilepsy. We experienced a case of 5-year-old boy who had unusual arousal and irritability every night for 3 years and had sharp & wave discharges from frontal lobe region in long-term video-EEG monitoring, who was suspected as an autosomal dominant nocturnal frontal lobe epilepsy. We report a case with a brief review of literatures.

Keyword

Autosomal dominant nocturnal frontal lobe epilepsy; Long-term video-EEG monitoring

MeSH Terms

Arousal
Carbamazepine
Child, Preschool
Epilepsies, Partial
Epilepsy
Epilepsy, Frontal Lobe*
Frontal Lobe*
Humans
Male
Neuroimaging
Prognosis
Seizures
Wills
Carbamazepine