J Korean Ophthalmol Soc.
1995 May;36(5):890-895.
A Case of Rieger's Syndrome Associated with Controlled Glaucoma
- Affiliations
-
- 1Department of Ophthalmology, School of Medicine, Soonchunhyang University, Chunan, Korea.
- 2Dr. Kim's Eye Clinic, Sung-nam, Korea.
Abstract
- Rieger's syndrome is a rare autosomal dominant developmental anomaly characterized by ocular and systemic abnomalities. These disorders are typically bilateral and usually diagnosed at birth or in the childhood. The most common ocular defects are hypoplasia of the iris, a prominent Schwalbe's line with iris strands and corectopia. A large number of patients have glaucoma due to devel-opmental defects of the anterior chamber angle structure. The authors experienced a case of Rieger's syndrome which was found in 31-year-old female, who had characteristic ocular and other systemic abnormalities. Associated glaucoma was well controlled by filtering surgery.
