Korean J Otolaryngol-Head Neck Surg.  2005 Dec;48(12):1526-1529.

Cerebellopontine Angle Kaposiform Hemangioendothelioma: A Case Report

• Oh SH
• Kim HM
• Park MH
• Jeon YK

Abstract

Hemangioendothelioma (HE) is an uncommon vascular neoplasm, and its intracranial occurrence is extremely rare, especially in the pediatric age group. The authors report a 7-month-old male patient with kaposiform HE who presented with left-sided facial paralysis and hearing loss. Initial magnetic resonance imaging (MRI) revealed a small lesion that filled the internal auditory meatus and exhibited the neuroimaging features of a vestibular schwannoma (VS). Six months later, follow-up MRI showed markedly enlarged mass. Biopsy disclosed kaposiform HE. After vascular embolization, partial resection was performed via transmastoid approach due to massive bleeding, followed by medical treatment with steroid and interferon-alpha. The tumor nearly disappeared 6 months after medical treatment. To our knowledge, it is a first reported case of kaposiform HE mimicking a VS in the cerebellopontine angle (CPA) area. A proper diagnosis is important because its treatment differs dramatically from that of VS. So, we report this case with a literature review.

Keyword

Kaposiform hemangioendothelioma; Cerebellopontine angle; Methylprednisolone; Interferon-alpha; Infant

MeSH Terms

Biopsy
Cerebellopontine Angle*
Diagnosis
Facial Paralysis
Follow-Up Studies
Hearing Loss
Hemangioendothelioma*
Hemorrhage
Humans
Infant
Interferon-alpha
Magnetic Resonance Imaging
Male
Methylprednisolone
Neuroimaging
Neuroma, Acoustic
Vascular Neoplasms
Interferon-alpha
Methylprednisolone