J Korean Pediatr Soc.  1996 Feb;39(2):280-286.

A Case of Tuberous Sclerosis Complex Developing with Subependymal Giant-Cell Astrocytoma and Hydrocephalus

• Chung KH
• Kim WS

Abstract

The subependymal giant-cell astrocytoma, a key feature of the tuberous sclerosis complex, has been reported in patients without obvious features of this condition. The tumor is a rare cerebral glioma that characteristically arise in the wall of lateral ventricle and as an intraventricular mass, causing hydrocephalus by obstruction of the foramen of Monro. We experienced a case of tuberous sclerosis in 9-year-old male patient who presented typical clinical manifestations and cortical tuber, subependymal giant-cell astrocytoma developing with hydrocephalus. Diagnosis was confirmed by brain CT and MRI. We applied surgical resection to remove the mass. Brief review and related literatures were also presented.

Keyword

Subependymal giant-cell astrocytoma; Tuberous Sclerosis Complex

MeSH Terms

Astrocytoma*
Brain
Cerebral Ventricles
Child
Diagnosis
Glioma
Humans
Hydrocephalus*
Lateral Ventricles
Magnetic Resonance Imaging
Male
Tuberous Sclerosis*