J Korean Neurosurg Soc.  1991 Mar;20(1-3):116-123.

Metastatic Alveolar Soft Part Sarcoma

• Park SH
• Lee KH
• Rhim HK
• Lee KW
• Shin HS
• Kang G
• Shin BC

Abstract

A case of metastatic alveolar soft part sarcoma is presented with clincal, pathological and radiological features. Alveolar soft part sarcoma is a rare soft-tissue neoplasm that is malignant and invariably fatal. It was first described and named by Christopherson, et al. in 1952. Since 1952 numerous examples of this tumor have been reported and have been studied with the electron microscope, but there is still considerable uncertainty as to the exact histogenesis of the tumor. Most cases occur in young females involving the lower extrimities especially in the right side. The most initial presenting symptom is a slowgrowing painless mass and the principal metastatic sites are the lungs, followed by the brain and skeleton. Cerebral metastasis, in fact, may be the first manifestation of the disease. Treatment is radical surgical excision but radiotherapy and chemotherapy are less effective. We present the reported case of metastatic alveolar soft pat sarcoma with electron microscopic findings.

Keyword

Alveolar soft part sarcoma; Painless mass; Metastasis; Radical excision

MeSH Terms

Brain
Drug Therapy
Female
Humans
Lung
Neoplasm Metastasis
Radiotherapy
Sarcoma
Sarcoma, Alveolar Soft Part*
Skeleton
Uncertainty