Korean J Thorac Cardiovasc Surg.  2000 Dec;33(12):963-967.

Surgical Management of Critical Pulmonary Stenosis: A case report

• Jung TY
• Ban DG
• Kim H
• Kim YH
• Chung WS
• Kang JH
• Jee HO
• Lee CB
• Kim NS
• Seoh JK

Abstract

Although pulmonary valvular stenosis with intact ventricular septum is a common congenital abnormality, critical pulmonary stenosis of its severe form in the neonate is rare and highly fatal. With the development of percutaneous balloon valvuloplasty, surgical treatment is even more rare. This report is on a 2 day old male neonate with a critical pulmonary stenosis with intact ventricular septum who suffered from severe cyanosis and hypoxemia. Oxygen was inhalated and Prostaglandin E1 was infused initially and then arterial PO2 was increased from 19 mmHg to 54 mmHg. Percutaneous balloon valvuloplasty was attemped; however, the guidewire could not pass through the stenotic pulmonary valve, and during the procedure right ventricular perforation was suspected due to the presence of dye in the pericardial space. Emergency transarterial pulmonary valvotomy was performed using normothermic cardiopulmonary bypass. Postoperatively, the patient was in fair condition in the ICU and presently is in good condition at 6 months postoperative follow up.

Keyword

Pulmonary valve, stenosis; Infant, newborn

MeSH Terms

Alprostadil
Anoxia
Balloon Valvuloplasty
Cardiopulmonary Bypass
Congenital Abnormalities
Constriction, Pathologic
Cyanosis
Emergencies
Follow-Up Studies
Humans
Infant, Newborn
Male
Oxygen
Pulmonary Valve
Pulmonary Valve Stenosis*
Ventricular Septum
Alprostadil
Oxygen