J Korean Neurosurg Soc.
2002 Dec;32(6):599-602.
Atypical Teratoid/Rhabdoid Tumor in Central Nervous System: Report of 2 Cases
- Affiliations
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- 1Department of Neurological Surgery, Asan Medical Center, College of Medicine, University of Ulsan, Seoul, Korea. ysra@amc.seoul.kr
- 2Department of Pediatrics, Asan Medical Center, College of Medicine, University of Ulsan, Seoul, Korea.
- 3Department of Pathology, Asan Medical Center, College of Medicine, University of Ulsan, Seoul, Korea.
Abstract
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We report two cases of atypical teratoid/rhabdoid tumor(AT/RT) in the central nervous system. Primary central nervous system AT/RT is an extremely rare malignant tumor affecting infants and young children. These tumors have been diagnosed previously as primitive neuroectodermal tumors(PNETs) because AT/RT contains fields indistinguishable from classic PNETs. Separation of these two tumor types is crucial because the prognosis for AT/RT is poor even when treatment includes surgery with or without radiation therapy and/or chemotherapy. Clinical, radiological and histopathological features of AT/RT are presented.