Korean J Obstet Gynecol.
2003 Jan;46(1):184-187.
A case of McCune-Albright syndrome
- Affiliations
-
- 1Department of Obstetrics and Gynecology, College of Medicine, Catholic University, Seoul, Korea.
Abstract
-
McCune-Albright syndrome is a rare disease. It's triad is 1) precocious puberty, 2) fibrous dysplasia of bone and 3) caf-al-lait spots on skin. The cause is known as the mutation of subunit of G protein. Although there are some suggestions of treatment regimens including antiestrogen and GnRH agonist, at present, the accurate management is not known. We have experienced a case of McCune-Albright syndrome who has precocious puberty and fibrous dysplasia without caf-al-lait spot, and we present the case with a review of related literatures.