J Cardiovasc Ultrasound.  2011 Dec;19(4):199-202. 10.4250/jcu.2011.19.4.199.

Rapidly Progressive Cardiac Manifestation of Behcet's Disease Involving Conduction System and Aortic Valve

• Yu JS
• Cho EJ
• Ji EH
• Kwon HS
• Kim JS
• Choi KY
• Kwon BJ
• Kim DB
• Jang SW
• Kim JH

• KMID: 1980383
• DOI: http://doi.org/10.4250/jcu.2011.19.4.199

Abstract

Cardiac conduction system impairment is a rare clinical manifestation of Behcet's disease. We report a patient who showed 1st degree atrioventricular block at first presentation, and showed aggravated finding of 3rd degree atrioventricular block on five months later. His cardiac manifestation finally developed to acute severe aortic regurgitation on six months later from his first cardiac manifestation. We observed this rapid progression during 6 months and successfully improved symptom and disease severity of the patient with treatment targeting Behcet's disease.

Keyword

Behcet's disease; Atrioventricular conduction system; Aortic regurgitation

MeSH Terms

Aortic Valve
Aortic Valve Insufficiency
Atrioventricular Block
Humans

Figure

• 

  Fig. 1 A: ECG finding of 1st admission on 6 months ago when patient complaint of chest pain shows 1st degree AV block. B: ECG finding of 1 month ago when patient complaint of 2 times of syncope shows complete AV block. C: ECG finding when patients was complaint severe dyspnea on emergency room shows 74 beat per minute of well functioning pacemaker with ventricular pacing beats of P wave tracing. ECG: electrocardiogram, AV: atrioventricular.

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  Fig. 2 A and B: TTE findings of 1 month ago when patient complaint of 2 times of syncope in parasternal long axis (A) and apical 5 chamber view (B) show aortic valve regurgitation of mild degree. C and D: On the TTE findings when patients was complaint severe dyspnea on emergency room shows severe aortic valve regurgitation in parasternal long axis (C) and apical 5 chamber view (D). E: On TEE examination, aortic valve thickening and billowing with redundant cusp (white arrows) is noted. F and G: The follow-up TTE on 1 year after open heart surgery showed no AR or aortic dilatation with normal LV function and dimension in parasternal long axis (F) and apical 5 chamber view (G). TTE: transthoracic echocardiography, TEE: transesophageal echocardiography, AR: aortic valve regurgitation, LA: left atrium, LV: left ventricle, Ao: Aorta.

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