Korean J Otorhinolaryngol-Head Neck Surg.  2015 Jul;58(7):509-513. 10.3342/kjorl-hns.2015.58.7.509.

A Case of Cochlear Implantation in Neurofibromatosis Type II

• Oh SJ
• Park JH
• Yi KI
• Goh EK

• KMID: 1964254
• DOI: http://doi.org/10.3342/kjorl-hns.2015.58.7.509

Abstract

Patients with neurofibromatosis type 2 (NF2) develop bilateral vestibular schwannomas that can cause binaural progressive hearing loss in most individuals. Auditory rehabilitation for bilateral profound sensorineural hearing loss in patients with NF2 poses a great therapeutic challenge. An auditory brainstem implantation may be an option after tumor excision, but its hearing results are still relatively unsatisfactory. A cochlear implantation (CI) may be another option in those cases where the cochlear nerve has been left intact after tumor excision or in those cases that have been kept stable after treating with Gamma-Knife. Here we report a case of undergoing CI after having been treated with Gamma-Knife in NF2 and showing improved open-set speech perception.

Keyword

Cochlear implantation; Gamma Knife radiosurgery; Neurofibromatosis 2

MeSH Terms

Auditory Brain Stem Implantation
Auditory Brain Stem Implants
Cochlear Implantation*
Cochlear Implants*
Cochlear Nerve
Hearing
Hearing Loss
Hearing Loss, Sensorineural
Humans
Neurofibromatosis 2*
Neuroma, Acoustic
Radiosurgery
Rehabilitation
Speech Perception