J Korean Neurol Assoc.
1990 Dec;8(2):372-377.
A Case of Multifocal Fibrosclerosis with CNS Involvement
- Affiliations
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- 1Department of Neurology, Hanyang University, Korea.
- 2Department of Internal Medicine, Hanyang University, Korea.
Abstract
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Multifocal fibrosclerosis, a rare disorder, has no known etiology and is considered to be a systemic illness manifested by combinations of fibrosing process of multiple areas such as mediastinal fibrosis, retroperitoneal fibrosis, orbital pseudotumor, sclerosing cholangitis, and Reidel's thyroiditis. We have experienced a 49-year-old man with pseudotumor of the orbit, sclerosing cholangitis, and CNS involvements included unrecognized meningitis and suspicious CNS vasculitis. The patient showed clinical improvement with corticosteroid therapy.