J Korean Neurol Assoc.  1990 Dec;8(2):372-377.

A Case of Multifocal Fibrosclerosis with CNS Involvement

Affiliations
  • 1Department of Neurology, Hanyang University, Korea.
  • 2Department of Internal Medicine, Hanyang University, Korea.

Abstract

Multifocal fibrosclerosis, a rare disorder, has no known etiology and is considered to be a systemic illness manifested by combinations of fibrosing process of multiple areas such as mediastinal fibrosis, retroperitoneal fibrosis, orbital pseudotumor, sclerosing cholangitis, and Reidel's thyroiditis. We have experienced a 49-year-old man with pseudotumor of the orbit, sclerosing cholangitis, and CNS involvements included unrecognized meningitis and suspicious CNS vasculitis. The patient showed clinical improvement with corticosteroid therapy.


MeSH Terms

Cholangitis, Sclerosing
Fibrosis
Humans
Meningitis
Middle Aged
Orbit
Orbital Pseudotumor
Retroperitoneal Fibrosis
Thyroid Gland
Thyroiditis
Vasculitis, Central Nervous System
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