J Korean Soc Plast Reconstr Surg.  2001 Jul;28(4):428-430.

Treatment of Barraquer-Simons Syndrome using Autologous Fat Graft

• Ahn MW
• Cho JW

Abstract

Barraquer-Simmons syndrome, also known as cephalothoracic lipodystrophy, is an uncommon disorder of unknown origin. Patients with this syndrome lose their subcutaneous fat of face and it progresses to the thoracic region. Simultaneously, the accumulation of subcutaneous fatty tissue in lower extremity occurs. The onset of this syndrome is known to be in their teens and patients are mainly female. The progression of this condition stops spontaneously in their early twenties. Twenty percents of patients show nephropathy with complement disorder which aggravates the prognosis. We present a 34-year-old female with typical features of this syndrome. This patients was treated with autologous free fat graft harvested from the gluteal area. The donor and recipient site healed uneventfully and the result was comparatively satisfactory. Autologous fat graft method is easy to perform, allows fast recovery with minimal donor site morbidity and is a useful method for the patients with Barraquer-Simmons syndrome.

Keyword

Barraquer-Simons syndrome; Fat graft; Facial atrophy

MeSH Terms

Adipose Tissue
Adolescent
Adult
Complement System Proteins
Female
Humans
Lipomatosis, Multiple Symmetrical
Lower Extremity
Prognosis
Subcutaneous Fat
Tissue Donors
Transplants*
Complement System Proteins