Korean J Thorac Cardiovasc Surg.  2007 Dec;40(12):867-870.

Pulmonary Thromboendarterectomy for Chronic Thromboembolic Pulmonary Hypertension in a Patient with Antiphospholipid Syndrome and Systemic Lupus Erythematosus

• Kang PJ
• Lee JW
• Kim JW

Abstract

Antiphospholipid syndrome (APS) is defined as venous and/or arterial thromboses, recurrent fetal losses, thrombocytopenia in combination with repeatedly positive tests for the lupus anticoagulant (LAC), and anticardiolipin antibodies (aCL). The pulmonary manifestations in APS are relatively rare. We report a rare case of antiphopholipid syndrome with systemic lupus erythematosus in a patient who presented with pulmonary hypertension secondary to a chronic pulmonary thromboembolism. A bilateral thromboendarterectomy was performed satisfactorily and the incision was extended to the left intrapleural pulmonary artery.

Keyword

Pulmonary embolism; Thromboembolism; Thromboendarterectomy; Antiphospholipid syndrome; Systemic lupus eruthematosus

MeSH Terms

Antibodies, Anticardiolipin
Antiphospholipid Syndrome*
Endarterectomy*
Humans
Hypertension, Pulmonary*
Lupus Coagulation Inhibitor
Lupus Erythematosus, Systemic*
Pulmonary Artery
Pulmonary Embolism
Thrombocytopenia
Thromboembolism
Thrombosis
Antibodies, Anticardiolipin
Lupus Coagulation Inhibitor