Korean J Perinatol.  2014 Mar;25(1):22-26. 10.14734/kjp.2014.25.1.22.

A Case of Intrauterine Lingual Cyst with Successful Delivery Assisting Ex Utero Intrapartum Treatment Procedure

• Hwang I
• Jung HR
• Bae JG

• KMID: 1917229
• DOI: http://doi.org/10.14734/kjp.2014.25.1.22

Abstract

Congenital lingual cyst is rare and there has been no prior case report about prenatally detected lingual cyst in Korea. When a huge oral cyst is observed at prenatal period and can cause life-threatening airway obstruction at birth, ex utero intrapartum treatment (EXIT) procedure is needed to secure the airway. Herein we present a baby with a prenatally detected huge oral cyst. He was delivered safely assisting EXIT procedure and underwent an operation for resection of the cyst from his tongue. The oral cyst was diagnosed as a lingual cyst with rare histologic type consisting mixed gastrointestinal and respiratory epithelium.

Keyword

Lingual cyst; Ex utero intrapartum treatment procedure; Congenital cyst; Oral cavity; Tongue

MeSH Terms

Airway Obstruction
Korea
Mouth
Parturition
Respiratory Mucosa
Tongue

Figure

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  Fig. 2. A large lingual cyst with risk of respiratory obstruction is present in oral cavity.

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  Fig. 1. Ultrasonography at 26 weeks of gestational age shows a large cystic lesion in oral cavity of fetus (A). MRI at 32 weeks of gestational age also shows a large simple cystic mass (34×31×27 mm, arrow) without solid portion or septal formation (B).

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  Fig. 3. The cyst is consisted mixed gastrointestinal and respiratory epithelium. Cystic lining cells are included gastrointestinal cells such as mucus, parietal or chief cells (A, HE stain, × 200). Cystic lining cells are also included ciliated pseudostratified columnar cells (respiratory epithelium) and squamous cells (B, HE stain, ×200).

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