Korean J Thorac Cardiovasc Surg.  2002 Apr;35(4):303-306.

Biventricular Repair of Critically Ill Neonate with Ebstein's Anomaly: Report of 1 case

• Kong JH
• Kim WH
• Ryu JW
• Lee SK
• Baek MJ
• Lim C
• Kim SC
• Oh SS
• Na CY
• Kim SJ
• Park YK
• Kim CW

Abstract

Patients with severe Ebstein's anomaly showing in the neonatal period, represent progressive cardiac enlargement with pulmonary hypoplasia and functional pulmonary atresia with patent ductus arteriosus-dependent pulmonary circulation. Biventricular repair in these patients had been mostly unsuccessful except for Starnes' procedure that converts the anatomy to single ventricle physiology for Fontan procedure. A 4-days old male was admitted with the diagnosis of severe Ebstein's anomaly with anatomic pulmonary atresia and severe cardiac enlargement. He successfully underwent biventricular repair with vertical plication method of atrialized right ventricle, tricupid annuloplasty, transannular right ventricular outflow tract reconstruction, atrial septal defect patch closure with fenestration, and right atrial reduction angioplasty. Postoperatively, cardiothoracic ratio was significantly reduced and mild tricuspid regurgitation was remnant in echocardiography. The patient is currently 10 months old and is fully active without restrictions.

Keyword

Ebstein's anomaly; Neonate; Surgery method

MeSH Terms

Angioplasty
Critical Illness*
Diagnosis
Ebstein Anomaly*
Echocardiography
Fontan Procedure
Heart Septal Defects, Atrial
Heart Ventricles
Humans
Infant
Infant, Newborn*
Male
Physiology
Pulmonary Atresia
Pulmonary Circulation
Tricuspid Valve Insufficiency