Korean J Pediatr Gastroenterol Nutr.  2001 Apr;4(1):113-119.

A Case of Mesenchymal Hamartoma Associated with Biliary Atresia

Affiliations
  • 1Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea.
  • 2Department of Radiology, Seoul National University College of Medicine, Seoul, Korea.
  • 3Department of Pathology, Seoul National University College of Medicine, Seoul, Korea.

Abstract

Mesenchymal hamartoma is an uncommon benign tumor usually found in childhood, especially during the first two years of life. The tumor consists of a solid component and multiple cyst. Without treatment, these lesions can grow to an enormous size. We experienced a case of mesenchymal hamartoma which was found incidentally, in a 8 month old girl who had ascending cholangitis after Kasai operation due to biliary atresia. On abdominal ultrasonography and CT, there was a well-defined homogeneous small echogenic mass in the right lobe of the liver with cirrhosis. Five months later, she underwent liver transplantation. Gross picture of the resected liver showed a dark greenish pigmented solid mass in the right lobe of the cirrhotic liver. Microscopic findings showed reactive mesenchyma and epithelial overgrowth.

Keyword

Mesenchymal hamartoma; Liver; Biliary atresia; Infant

MeSH Terms

Biliary Atresia*
Cholangitis
Female
Fibrosis
Hamartoma*
Humans
Infant
Liver
Liver Transplantation
Mesoderm
Ultrasonography
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