Korean J Radiol.  2009 Aug;10(4):416-419. 10.3348/kjr.2009.10.4.416.

Nasal Chondromesenchymal Hamartoma: CT and MR Imaging Findings

• Kim JE
• Kim HJ
• Kim JH
• Ko YH
• Chung SK

• KMID: 1777273
• DOI: http://doi.org/10.3348/kjr.2009.10.4.416

Abstract

We report CT and MR imaging findings for a case of nasal chondromesenchymal hamartoma occurring in a 19-month-old boy. A nasal chondromesenchymal hamartoma is a rare benign pediatric hamartoma that can simulate malignancy. Although rare, knowledge of this entity is essential to avoid potentially harmful therapies.

Keyword

Nose, neoplasms; Paranasal sinus, neoplasms; Paranasal sinus, CT; Paranasal sinus, MR

MeSH Terms

Hamartoma/*diagnosis
Humans
Infant
Magnetic Resonance Imaging
Male
Nose Neoplasms/*diagnosis
Tomography, X-Ray Computed

Figure

• 

  Fig. 1 Case of nasal chondromesenchymal hamartoma in 19-month-old boy. A. Axial postcontrast CT scan shows well-defined, minimally enhancing, expansile mass in left nasal cavity, extending to anterior ethmoid sinus. Thinning of adjacent bones caused by pressure remodeling is observed without evidence of frank destruction. Nasal septum is also displaced to right. Also noted is opacification of left maxillary sinus due to obstruction by mass. On precontrast CT scans, mass was isodense to cerebral cortex without evidence of intralesional calcification (not shown). B. Coronal T1-weighted MR image demonstrates homogeneously isointense mass, compared with cerebral cortex. C. Coronal fat-suppressed T2-weighted MR image demonstrates heterogeneously hyperintense mass, in relation to cerebral cortex, containing small area of bright signal intensity peripherally (arrow). Although lesion abuts orbit and anterior cranial base, direct extension of lesion to orbit and intracranial cavity is not evident. D. Coronal contrast-enhanced fat-suppressed T1-weighted MR image shows mild, diffuse heterogeneous enhancement of lesion. Small area of bright signal intensity seen on T2-weighted image is non-enhancing cystic component (arrow). Note fluid-filled left maxillary sinus on B-D. E. Photomicrograph shows tumor consisting of multiple chondromyxoid islands (I) in spindle cell stroma (Hematoxylin & Eosin staining, × 100).

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