Korean Circ J.  2008 Sep;38(9):491-494. 10.4070/kcj.2008.38.9.491.

A Case of Mitochondrial Myopathy With Cardiac Involvement

• Son SW
• Kim DB
• Kwon BJ
• Jang SW
• Cho EJ
• Park CH
• Kim DB
• Shin JY
• Rho TH
• Kim JH

• KMID: 1776350
• DOI: http://doi.org/10.4070/kcj.2008.38.9.491

Abstract

Mitochondrial myopathy is a disease caused by structural, biochemical or genetic disturbance of the mitochondria and this affects many organs, and it may also involve the cardiac muscles. We experienced a case of myocardial involvement in a 21 years old male patient with mitochondrial myopathy.

Keyword

Mitochondrial myopathies; Cardiomyopathies

MeSH Terms

Cardiomyopathies
Humans
Male
Mitochondria
Mitochondrial Myopathies
Myocardium

Figure

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  Fig. 1 Electron micrograph showed an increased number of abnormal mitochondria that contained paracrystalline structures (white arrow) in the subsarcolemmal area.

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  Fig. 2 Change of the electrocardiogram during 6 months. A: the initial electrocardiogram showed non-specific findings. B: 6 months later, the follow-up electrocardiogram showed newly developed T-wave inversion in the limb leads (III, aVF) and the precordial leads (V1-V4).

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