J Korean Pediatr Soc.  1993 Jun;36(6):865-869.

Two cases of Dyke-Davidoff-Masson syndrome

• Park DG
• Park JH
• Yoo KH
• Choung JT
• Son CS
• Tockgo YC

Abstract

Dyke-Davidoff-Masson syndrome is a rare disorder which developed hemiatrophy of brain, enlargement of ventricles and prominent pneumatization of petrous pyramid of the temporal bone. It manifests hemiparesis, varying type seizure, and mental retardation. We experienced two cases of Dyke-avidoff-Masson Syndrome, in a 6/12 year-old boy and a 1, 10/12 year-old girl who were admitted to our department of pediatrics, because of convulsion and hemiparesis The brain CT scan showed marked dilatation of lateral ventricle, prominent sylvian fissure and cortical sulci. So we report two cases of Dyke-Davidoff-Masson syndrome with review of literature.

Keyword

Cerebral hemiatrophy; Hemiparesis

MeSH Terms

Brain
Dilatation
Female
Humans
Intellectual Disability
Lateral Ventricles
Male
Paresis
Pediatrics
Petrous Bone
Seizures
Temporal Bone
Tomography, X-Ray Computed