Korean Circ J.  1976 Dec;6(2):25-31. 10.4070/kcj.1976.6.2.25.

Surgical Treatment of Ebstein Anomaly: One Case Report

• Song YJ
• Lee NS
• Kim HM

• KMID: 1667924
• DOI: http://doi.org/10.4070/kcj.1976.6.2.25

Abstract

In the Dept. of Thoracic Surgery, Korea University Hospital, Preoperative diagnosis as Ebstein anomaly was made on the 11-year old female through the preoperative examination including right cardioangiography and the Glenn Operation was performed to this patients as palliative treatment. During closure of the thoracic wall just after the anastomosis of S.V.C. and right pulmonary artery, sudden cardiac arrest developed. One day later after death, autopsy was performed in order to confirm the pathologic anatomy of the cardiac anomaly and to clarify the cause of death. Pathologic anatomy of the heart revealed the huge dilatation of right atrium, Patent Foramin Ovale, and the deformed and descended posterior and the septal leaflets of tricuspid value by which right ventricle was devided into the atrialized and the functional portion. The diagnosis of the autopsy showed (1) Ebstein Anomaly (2) bilateral total atelectasis of the lung, (3) multiple petechial hemorrhage and edema of the myocardium, brain and liver due to acute hypoxia, (4) fibrocaseous tuberculosis of the liver and tuberculous pericholangitis.

MeSH Terms

Anoxia
Autopsy
Brain
Cause of Death
Child
Death, Sudden, Cardiac
Diagnosis
Dilatation
Ebstein Anomaly*
Edema
Female
Heart
Heart Atria
Heart Ventricles
Hemorrhage
Humans
Korea
Liver
Lung
Myocardium
Palliative Care
Pulmonary Artery
Pulmonary Atelectasis
Thoracic Surgery
Thoracic Wall
Tuberculosis