J Korean Pediatr Soc.  1980 May;23(5):417-422.

A cases of Congenital Nephrogenic Diabetes Insipidus with Bilateral Hydronprosis

• Sohn YM
• Lee C
• Kim PK
• Yun DJ

Abstract

A 13 year old boy was diagnosed as primary nephrotic diabetesinsipidus, whose symptom has been devloped from 3 years of age, subsequetly he developed bilateral hydronephrosis and neurogenic bladder. His pedigree could be explored 5 generations and represented inheritace as X-linked recesslive transmission, He was treated with indomethacin 2mg/Kg/day plus chlorothiazid 500mg/dau and this new method shows markedly decreased urine outpur and increased urine osmolarity.

MeSH Terms

Adolescent
Diabetes Insipidus, Nephrogenic*
Family Characteristics
Humans
Hydronephrosis
Indomethacin
Male
Osmolar Concentration
Pedigree
Urinary Bladder, Neurogenic
Indomethacin