Korean J Dermatol.  1975 Jun;13(2):151-155.

A Case of Lipodystropha Centrifugalis Abdominalis Infantilis

• Lee KW
• Cho BK
• Houh W

Abstract

Lipodystrophia centrifugalis ahdominalis infantilis(LCAI), an atypical form of progressive lipodystrophy, is a diseaee named by Imamura et al in 1971, and reported a few cases in japan. We report a case who has diagnosed as LCAI. The patient ia 5 and half year old boy. He had 2cm by 7cm sized, linear depressed leaion with surrounding erythema on the right inguinal region which was noticed 5 months prior to first diagnosis. There was no family history, no physical abnormality except skin lesion. Cornplete blood cell count, urinalysis, stool examination, liver function test and chest X-ray were within normal limit. Biopsy specimens from the depressed lesion and surrounding erythematous area revealed slight atrophy of the epidermis, a mild lymphocyte infiltration around the vesaels and eccrine glands in the upper part of derrnis, markedly decreased amount of subcutaneous adipoae tissue with mild lymph- ocyte infiltration in depressed area and marked lymphocyte infiltration, intermingled with histiocyte in surrounding erythematous area, but normal amount of adipase tissue.

MeSH Terms

Atrophy
Biopsy
Blood Cell Count
Diagnosis
Eccrine Glands
Epidermis
Erythema
Histiocytes
Humans
Japan
Lipodystrophy
Liver Function Tests
Lymphocytes
Male
Skin
Thorax
Urinalysis