Korean J Dermatol.
2000 Oct;38(10):1382-1384.
A Case of Job's Syndrome
- Affiliations
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- 1Department of Dermatology, College of Medicine, Inha University, Inchon, Korea.
Abstract
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The Job's syndrome is a relatively rare primary immunodeficiency disorder characterized by recurrent staphylococcal infection and abscess formation, defective neutrophil chemotaxis, and markedly elevated serum IgE level. Clinical features are atopiclike dermatitis, furunculosis, paronychia, pulmonary bacterial pneumonia etc. We reported a case of Job's syndrome in a 12-year-old girl who had recurrent pneumonia, scaly pruritic dermatitis, fissured tongue, and nail dystrophy with elevated serum IgE level.