J Korean Endocr Soc.  2007 Oct;22(5):371-375. 10.3803/jkes.2007.22.5.371.

A Case of Adrenal Angiomyolipoma

• Kim SK
• Lee WS
• Jeong GH
• Kim HK
• Myung DS
• Chung JO
• Chung DJ
• Chung MY
• Kang HC

• KMID: 1523108
• DOI: http://doi.org/10.3803/jkes.2007.22.5.371

Abstract

An angiomyolipoma is a benign mesenchymal neoplasm that typically occurs in the kidney of patients with tuberous sclerosis. Extrarenal angiomyolipomas are uncommon, and the adrenal gland is an extremely rare site for the tumor. An incidental adrenal mass is the usual presentation of an adrenal angiomyolipoma, as most of the tumors are hormonally inactive. Recently we experienced one case of a right adrenal angiomyolipoma that presented with an adrenal incidentaloma. To the best of our knowledge, this is the first case of an adrenal angiomyolipoma described in the Korean medical literature. We report the case with a special emphasis on the differential imaging findings of fat-containing adrenal tumors.

Keyword

Adrenal gland neoplasm; Angiomyolipoma

MeSH Terms

Adrenal Gland Neoplasms
Adrenal Glands
Angiomyolipoma*
Humans
Kidney
Tuberous Sclerosis

Figure

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  Fig. 1 Abdominal ultrasonogram shows a widening of hepatorenal recess and suspicious echogenic lesion (arrowheads).

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  Fig. 2 Abdominal CT scans. A, An about 9 cm sized low-density mass in right suprarenal region (arrowhead). B, Numerous vessels and mild contrast enhancement after injection of contrast agent (arrowheads).

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  Fig. 3 Abdominal MRI scans. A, T1-weighted axial scan reveals a right adrenal mass with high signal intensity. B, Moderate high signal intensity is seen on T2-weighted image. C, The anatomical relationship between the mass and surrounding organs is well shown in coronal scan.

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  Fig. 4 Gross and histologic finding of the mass. A, The cut surface of the tumor shows the fatty nature of the mass. B, Histology confirms the diagnosis of angiomyolipoma. The tumor is consisted of abundant fatty tissue, vessels and smooth muscles (H&E stain, ×100). C and D, Immunohistochemical stain shows positive finding for actin and HMB-45 (IHC, ×400).

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