Korean J Pediatr.  2008 Jan;51(1):98-101. 10.3345/kjp.2008.51.1.98.

Primary leiomyosarcoma of the chest wall in a child: a case report

• Choi JH
• Chung DC
• Lee MJ

• KMID: 1487167
• DOI: http://doi.org/10.3345/kjp.2008.51.1.98

Abstract

Leiomyosarcoma is an uncommon soft tissue sarcoma of mesenchymal cell origin, which shows smooth muscle differentiation. Leiomyosarcoma is seldom found in the pediatric population, and accounts for fewer than 2% of all soft tissue sarcomas. Leiomyosarcoma of the chest wall is extremely rare in children. We report here a case of an 8-year-old boy with a primary leiomyosarcoma that was incidentally found as a rib mass. The patient underwent a complete resection for a suspected osteochondroma diagnosed by a three-dimensional chest computed tomography examination. Pathological findings of the mass revealed intersecting fascicles of spindle cells showing cigar-shaped nuclei, inconspicuous nuclear pleomorphism and occasional mitotic figures in the background of a suspected osteochondroma of the rib. This report documents the first description of a leiomyosarcoma possibly arising in an osteochondroma of the rib in a child.

Keyword

Leiomyosarcoma; Chest wall; Rib; Osteochondroma; Child

MeSH Terms

Child
Humans
Leiomyosarcoma
Muscle, Smooth
Osteochondroma
Ribs
Sarcoma
Thoracic Wall
Thorax