J Korean Assoc Maxillofac Plast Reconstr Surg.
2009 Sep;31(5):440-443.
Oral Manifestation and Treatment in Cleidocranial Dysplasia Patient: A Case Report
- Affiliations
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- 1Department of oral&Maxillofacial Surgery, College of Dentistry, Kyungpook National University, Daegu, Korea. kimcs@knu.ac.kr
- 2Department of Dentistry, Youngnam University Medical center, Korea.
- 3Department of Dentistry, Ulsan University Hospital, Korea.
Abstract
- Cleidocranial dysplasia(CCD) is a rare syndrome usually caused by an autosomal dominant gene or no apparent genetic cause. The skull is large and short with marked bossing of the frontal bone. Closure on the fontanelles and sutures is delayed. The clavicle may be unilaterally or bilaterally aplastic. Oral manifestations include multiple impacted permanent teeth, prolonged retention of primary teeth and multiple supernumerary teeth. There are many difficulties in the early diagnosis of CCD because a majority of the craniofacial abnormalities becomes obvious only during adolescence. Late diagnosis produce occlusional&psychological problem. Therefore early detection and treatment of CCD can reduce the period and the extent of orthodontic and surgical interventions. We experienced CCD patient with multiple supernumerary teeth and will report it with the literature review.
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