Korean J Audiol.  2011 Sep;15(2):90-93.

A Case of External Auditory Canal Stenosis in Langerhans Cell Histiocytosis

• Sohn I
• Lee HB
• Kim SY
• Choung YH

Abstract

Langerhans cell histiocytosis (LCH) refers a group of disorders of the reticuloendothelial system characterized by a proliferation of histiocytes, which includes eosinophilic granuloma, Lettere-Siwe diseases, and Hand-Schuler Christian disease. The clinical presentation of LCH depends on the site of involvement. It can range from multifocal lesions to a solitary lesion. Tissues characteristically involved in LCH are bone, skin, lung, liver, spleen, bone marrow, lymph nodes and the hypothalamic-pituitary region, although the involvement of other organs such as the bowel can occur. We experienced a case of external auditory canal stenosis in LCH of multiple organ involvement in a 28-year-old male, and report it with a review of the relevant literature.

Keyword

Langerhans cell histiocytosis; Temporal bone; External auditory canal; Stenosis

MeSH Terms

Adult
Bone Marrow
Constriction, Pathologic
Ear Canal
Eosinophilic Granuloma
Histiocytes
Histiocytosis, Langerhans-Cell
Humans
Liver
Lung
Lymph Nodes
Male
Mononuclear Phagocyte System
Skin
Spleen
Temporal Bone